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Hybrid procedures for an infant with hypoplastic left heart syndrome with intact atrial septum

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An Invited Commentary to this article was published on 10 December 2013

Abstract

A boy, prenatally diagnosed as hypoplastic left heart syndrome (HLHS) with intact atrial septum (IAS) was successfully treated by hybrid procedures. He underwent emergent catheter atrial septostomy and stent insertion in the atrial septum on Day 1 and then underwent bilateral pulmonary artery banding, ductal stent insertion, modified Norwood operation, bidirectional Glenn’s operation and finally Fontan type operation at 2 years of age. Considering the presence of decompression pathway from the left atrium in HLHS with IAS, we should organize a treatment team for collaborative work and plan an appropriate treatment strategy before delivery. Although his clinical course has been uneventful until now, closer medical observation is warranted because he may have coexisting pulmonary disease.

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References

  1. Pigula FA, Vida V, del Nido P, Bacha E. Contemporary results and current strategies in the management of hypoplastic left heart syndrome. Semin Thorac Cardiovasc Surg. 2007;19:238–44.

    Article  PubMed  Google Scholar 

  2. Galantowicz M, Cheatham JP, Phillips A, Cua CL, Hoffman TM, Hill SL, et al. Hybrid approach for hypoplastic left heart syndrome: intermediate results after the learning curve. Ann Thorac Surg. 2008;85:2063–71.

    Article  PubMed  Google Scholar 

  3. Rychik J, Rome JJ, Collins MH, DeCampli WM, Spray TL. The hypoplastic left heart syndrome with intact atrial septum: atrial morphology, pulmonary vascular histopathology and outcome. J Am Coll Cardiol. 1999;34:554–60.

    Article  CAS  PubMed  Google Scholar 

  4. Taketazu M, Barrea C, Smallhorn JF, Wilson GJ, Hornberger LK. Intrauterine pulmonary venous flow and restrictive foramen ovale in fetal hypoplastic left heart syndrome. J Am Coll Cardiol. 2004;43:1902–7.

    Article  PubMed  Google Scholar 

  5. Malec E, Januszewska K, Kolcz J, Mroczek T. Right ventricle-to-pulmonary artery shunt versus modified blalock–taussig shunt in the Norwood procedure for hypoplastic left heart syndrome––influence on early and late hemodynamic status. Eur Cardiothorac Surg. 2003;23:728–34.

    Article  Google Scholar 

  6. Imoto Y, Kado H, Shiokawa Y, Minami K, Yasui H. Experience with the Norwood procedure without circulatory arrest. J Thorac Cardiovasc Surg. 2001;122:879–82.

    Article  CAS  PubMed  Google Scholar 

  7. Tworetzky W, McElhinney DB, Mohan Reddy V, Brook MM, Hanley FL, Silverman NH. Improved surgical outcome after fetal diagnosis of hypoplastic left heart syndrome. Circulation. 2001;103:1269–73.

    Article  CAS  PubMed  Google Scholar 

  8. Akintuerk H, Michel-Behnke I, Valeske K, Mueller M, Thul J, Bauer J, et al. Stenting of the arterial duct and banding of the pulmonary arteries: basis for combined Norwood stage I and II repair in hypoplastic left heart. Circulation. 2002;105:1099–103.

    Article  PubMed  Google Scholar 

  9. Eicken A, Gildein HP, Schreiber C, Balling G, Hess J. Stenting of a restrictive foramen ovale in a patient with hypoplastic left heart syndrome. Int J Cardiol. 2006;113:254–6.

    Article  PubMed  Google Scholar 

  10. Lowenthal A, Kipps AK, Brook MM, Meadows J, Azakie A, Moon-Grady AJ. Prenatal diagnosis of atrial restriction in hypoplastic left heart syndrome is associated with decreased 2-year survival. Prenat Diagn. 2012;32:485–90.

    Article  PubMed Central  PubMed  Google Scholar 

  11. Marshall AC, Levine J, Morash D, Silva V, Lock JE, Benson CB, et al. Results of in utero atrial septoplasty in fetuses with hypoplastic left heart syndrome. Prena Diag. 2008;28:1023–8.

    Article  Google Scholar 

  12. Pavlovic M, Acharya G, Huhta JC. Controversies of fetal cardiac intervention. Early Hum Dev. 2008;84:149–53.

    Article  PubMed  Google Scholar 

  13. Ishizaka T, Ohye RG, Suzuki T, Devaney EJ, Bove EL. Bilateral pulmonary artery banding for resuscitation in hypoplastic left heart. Ann Thorac Surg. 2003;75:277–9.

    Article  PubMed  Google Scholar 

  14. Luciani GB, Pessotto R, Mombello A, Mazzucco A. Hypoplastic left heart syndrome with restrictive atrial septal defect and congenital pulmonary lymphangiectasis. Cardiovasc Pathol. 1999;8:49–51.

    Article  CAS  PubMed  Google Scholar 

  15. Graziano JN, Heidelberger KP, Ensing GJ, Gomez CA, Ludomirsky A. The influence of a restrictive atrial septal defect on pulmonary vascular morphology in patients with hypoplastic left heart syndrome. Pediatr Cardiol. 2002;23:146–51.

    Article  CAS  PubMed  Google Scholar 

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Authors and Affiliations

  1. Department of Pediatrics, University of Yamanashi, Chuo-City, Japan

    Hiroaki Kise, Minako Hoshiai, Keiichi Koizumi & Yohei Hasebe

  2. Department of Surgery, University of Yamanashi, 1110 Shimokato, Chuo-City, Yamanashi, 409-3898, Japan

    Shoji Suzuki, Shigeaki Kaga, Shinya Motohashi & Masahiko Matsumoto

Authors
  1. Shoji Suzuki
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  2. Hiroaki Kise
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  3. Shigeaki Kaga
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  4. Minako Hoshiai
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  5. Keiichi Koizumi
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  6. Yohei Hasebe
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  7. Shinya Motohashi
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  8. Masahiko Matsumoto
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Correspondence to Shoji Suzuki.

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Suzuki, S., Kise, H., Kaga, S. et al. Hybrid procedures for an infant with hypoplastic left heart syndrome with intact atrial septum. Gen Thorac Cardiovasc Surg 63, 472–475 (2015). https://doi.org/10.1007/s11748-013-0304-7

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  • DOI: https://doi.org/10.1007/s11748-013-0304-7

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