Table 1

Clinical characteristics

AllEvent (+)Event (-)P value
Male, %14 (10)1 (4)13 (11)0.11
Body mass index22±322±322±30.88
WHO Class I/II/III/IV27/82/31/05/16/4/022/66/27/00.54
Disease duration, months1.
Antihypertensive drugs, %2 (1)0 (0)2 (2)0.16
Diuretic, %3 (2)1 (4)2 (2)0.59
Anticoagulants, %0 (0)0 (0)0 (0)
Respiratory function
%EFV1, %80±482±679±40.82
%FVC, %109±13113±15107±120.34
Baseline haemodynamics
HR, bpm68±1268±1067±120.67
Systolic BP, mm Hg123±20122±22123±190.93
Diastolic BP, mm Hg68±1068±1069±100.68
SpO2, %98±197±298±10.53
Post-6-minute walk haemodynamics
HR, bpm90±1792±1889±160.54
Systolic BP, mm Hg128±25129±22128±250.79
Diastolic BP, mm Hg66±1570±1965±140.22
SpO2, %96±396±296±30.80
6MW distance, m432±89451±94428±870.26
  • Data are presented as number of patients (percentage) and mean±SD.

  • BP, blood pressure; %DLCO, diffusing capacity for carbon monoxide; %FEV1, percent forced expiratory volume in 1 s; %FVC, percent forced vital capacity; HR, heart rate; MCTD, mixed connective tissue disease; SpO2, percutaneous oxygen saturation; SSc, systemic sclerosis.