Table 1

Baseline demographic and clinical characteristics

DemographicValue
Male (n,(%))54,(58%)
Age (years)30.2±8.8
ACHD follow-up (years)7.27±5.1
Total follow-up (years)2809
Average cardiac surgeries/procedures4.07±1.59
Clinical characteristic, n (%)
Fontan type
 Atriopulmonary28 (30.1)
 Lateral tunnel35 (37.6)
 Extracardiac29 (31.1)
AV regurgitation
 None/trivial41 (44.1)
 Mild31 (33.3)
 Moderate16 (17.2)
 Severe2 (2.2)
Systemic ventricle
 LV69 (74.2)
 RV21 (22.6)
Systolic dysfunction
 None50 (53.8)
 Mild31 (33.3)
 Moderate9 (9.7)
 Severe1 (1.1)
Medication, n (%)
 ASA27 (29.0)
 Warfarin49 (52.7)
 DOAC3 (3.2)
 LMWH2 (2.2)
 ACEi33 (35.5)
 BB29 (31.2)
 Digoxin11 (11.8)
 Diuretic16 (17.2)
 Amiodarone5 (5.4)
 Sotalol8 (8.6)
  • ACEi, angiotensin converting enzyme inhibitor; ASA, acetylsalicylic acid; AV, atrioventricular; BB, beta blocker; DOAC, direct oral anticoagulant; LMWH, low molecular weight heparin; LV, left ventricle; RV, right ventricle.