Table 4

Causes of death or HTX among the 284 Fontan patients

SLV(n=138)SRV(n=120)MIX(n=26)Total(n=284)
Postoperative complications*77115
Heart failure†111113
Sudden death‡1304
Failed Fontan§3104
Infection¶2103
Thrombosis**1102
Total1524241
  • *Various complications within 30 days of last surgery.

  • †Myocardial and/or valvar failure.

  • ‡Death occurring within minutes from any cause, including malignant tachyarrhythmias.

  • §See Definitions.

  • ¶Pneumonia, sepsis, gastroenteritis.

  • **Shunt thrombosis or thrombosis in Fontan circuit, myocardial infarction, stroke.

  • HTX, heart transplantation; MIX, mixed or indeterminate ventricular morphology; SLV, single left ventricular morphology; SRV, single right ventricular morphology.