Table 4

List of inherited heart diseases and relevant International Statistical Classification of Diseases and Related Health Problems codes (ICD-9-AM)

Inherited heart conditionICD diagnostic code and category
Arrhythmogenic right ventricular cardiomyopathyI42.8 Other cardiomyopathies
Bicuspid aortic valve diseaseQ23.83 Congenital bicuspid aortic valve
Brugada syndromeI49.8 Other specified cardiac arrhythmias
Catecholaminergic polymorphic ventricular tachycardiaI47.2 Ventricular tachycardia
Familial dilated cardiomyopathyI42.0 Dilated cardiomyopathy
Familial hypercholesterolaemiaE78.0 Pure hypercholesterolaemia
Familial restrictive cardiomyopathyI42.5 Other restrictive cardiomyopathy
Hypertrophic cardiomyopathyI42.1 Obstructive hypertrophic cardiomyopathy
I42.2 Other hypertrophic cardiomyopathy
Q24.89 Other specified congenital malformations of the heart
Left ventricular non-compactionI42.8 Other cardiomyopathies
I42.9 Cardiomyopathy, unspecified
Long QT syndromeR94.3 Abnormal results of cardiovascular function studies
Marfan syndromeQ87.4 Marfan syndrome