Baseline characteristics of 95 children undergoing ajmaline provocation testing
| BrS-positive result | BrS-negative result | p Value comparing positive vs negative | Total | |
|---|---|---|---|---|
| N | 19 | 76 | 95 | |
| Mean age (SD) | 11.87 (3.1) | 12.8 (3.37) | 0.266 | 12.55 (3.34) |
| Age range | 7.4–16.4 | 1.9–18.4 | 1.9–18.4 | |
| Indications Family history of BrS (n) | 13 | 33 | 0.08* | 45 (48%) |
| Family history of SCD (n) | 5 | 34 | 39 (41%) | |
| Symptomatic (n) | 1 | 8 | 9 (9%) | |
| Partial RBBB on ECG† | 7/16 (44%) | 23/71 (32%) | 0.3732 | 30/87 (34%) |
*χ2 Test (with Yates correction p=0.14). Comparison of positive test rates between those tested for family history of BrS and those tested for family history of sudden cardiac death (symptomatic group excluded due to small numbers).
†ECGs were unavailable in 12 cases, however available in three repeat tests.
BrS, Brugada syndrome; RBBB, right bundle branch block; SCD, sudden cardiac death.